Güncel Patoloji Dergisi
2019, Cilt 3, Sayı 3
Recent Developments in Interstitial Lung Diseases
1 Sağlık Bilimleri Üniversitesi, Atatürk Göğüs Hastalıkları ve Göğüs Cerrahisi Eğitim ve Araştırma Hastanesi, Tıbbi Patoloji Anabilim Dalı, ANKARA
DOI :
10.5146/jcpath.2019.56
Idiopathic interstitial pneumonia is a combination of histologically different amounts of fibrosis and inflammation. Therefore, a multidisciplinary
council decision is recommended for diagnosis. A guide for clinical diagnosis of idiopathic pulmonary fibrosis, including clinical, radiological
and histopathological data, has been published. In recent years, chronic hypersensitivity pneumonia has become prominent in the differential
diagnosis of idiopathic pulmonary fibrosis. Pleuroparenchymal fibroelastosis, autoimmune interstitial pneumonia, combined pulmonary
fibrosis and emphysema syndrome, fibrosing cryptogenic organized pneumonia, acute fibrinous and organized pneumonia are newly defined
entities. In many interstitial lung diseases, telomere related genetic changes have been described and genetic features of interstitial lung diseases
have been demonstrated.
Anahtar Kelimeler :
Interstitial lung disease, Classification, Idiopathic interstitial pneumonia, Pathology
